CPPD Crowned Dens Syndrome with clivus destruction: A case report

CPPD Crowned Dens Syndrome with clivus destruction: A case report

Sayed Ali, Michael Hoch, Vipulkumar Dadhania, Jasvir S. Khurana

Abstract


We report a case of CPPD crowned dens syndrome in an 87 year white old male with a known history of pseudogout, with clinical and radiological features characteristic of this syndrome. Interestingly, there was significant mass effect on the clivus, with clivus erosion and destruction, a finding that has not previously been described with this syndrome. The clinical and radiological characteristics of Crowned Dens syndrome, as well as CPPD are reviewed. We suggest that CPPD crowned dens syndrome may be included in the differential diagnosis when clivus destruction or erosion, in association with a soft tissue mass with calcification, is seen.


Keywords


Calcium pyrophosphate dihydrate deposition disease; dens; clivus



DOI: https://doi.org/10.3941/jrcr.v5i8.802