Saw Tooth Cardiomyopathy with Parachute Mitral Valve – An Unusual Association

Authors

  • Arathy Vijayan, DNB Department of Radiology, Narayana Institute of Cardiac Sciences, Bangalore
  • Richa Kothari, DNB Department of Radiology, Narayana Institute of Cardiac Sciences, Bangalore
  • Vimal Raj, FRCR Department of Cardiothoracic imaging, Narayana institute of cardiac sciences, Bangalore

DOI:

https://doi.org/10.3941/jrcr.5863

Abstract

Saw tooth cardiomyopathy (STC) is an extremely rare myocardial disorder, with fewer than 14 cases reported since its initial description in 2009. It is defined by distinctive myocardial projections resembling a saw tooth pattern on cardiac MRI. No consistent genetic or pathological abnormalities have been identified. Cardiac MRI with late gadolinium enhancement remains the diagnostic standard. Reported associations include apical aneurysm, patent foramen ovale, mitral valve prolapse, and myocardial bridging. We report a rare case of STC associated with a parachute mitral valve—an association not previously described—broadening the phenotypic spectrum of this under-recognized cardiomyopathy.

ECG of the child showing sinus rhythm with interpolated PVCs, normal PR interval and flat p waves

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Published

2025-12-24

Issue

Section

Cardiac Imaging