A Case of Craniofacial Polyostotic Fibrous Dysplasia

Authors

  • Justin Clark
  • William Keith Carson

DOI:

https://doi.org/10.3941/jrcr.v4i9.330

Keywords:

Fibrous Dysplasia, Polyostotic, Craniofacial, Optic Nerve Decompression

Abstract

We present the case of a patient with craniofacial polyostotic fibrous dysplasia. Polyostotic fibrous dysplasia is relatively rare and usually presents in late childhood/early adulthood.  It is occasionally associated with endocrine disorders such as McCune-Albright syndrome.  The benign pathology of this bone tumor belies its implications in the region of the skull base.  Craniofacial polyostotic fibrous dysplasia can have devastating complications depending on which ostia are involved, including vision loss.  Our patient was already beginning to experience visual field deficits from ischemic neuropathy.  He was treated surgically with optic nerve decompression; however, the efficacy of this approach is currently being debated.

Author Biographies

Justin Clark

LT, MC(FMF), USN

Resident

Department of Radiology, Naval Medical Center San Diego

William Keith Carson

LCDR, MC, USN

Department Head

Department of Radiology, US Naval Hospital Okinawa

Published

2010-09-01

Issue

Section

General Radiology