Incidental finding - the discovery of a bronchopulmonary foregut malformation through investigations for Crohn's disease

Incidental finding - the discovery of a bronchopulmonary foregut malformation through investigations for Crohn's disease

Humza Mahmood, Andrew Plumb, Roser Vega, Alastair Windsor

Abstract


Pulmonary sequestration (PMS) is a rare bronchopulmonary malformation. It has an incidence of between 0.15% to 1.7%. Likewise, cystic adenomatoid malformation (CCAM) is another relatively rare category of a bronchopulmonary malformation with a reported incidence of between 1 in 25,000 to 1 in 35,000. Moreover, a bronchopulmonary malformation with features allied to both of these forms is considered an even rarer entity. In general, bronchopulmonary malformations present with a range of non-specific symptoms. Radiological features can be non-specific yet distinctive when related to clinical features. Ultimately, definitive diagnosis depends upon histological assessment of lung tissue. We present an adult female with radiological features of both pulmonary sequestration and cystic adenomatoid malformation. This was an incidental finding unrelated to the patients presenting complaint. This case highlights the importance of using a structured and systematic approach when interpreting medical imagery.

Keywords


bronchopulmonary foregut malformation; pulmonary sequestration; congenital cystic adenomatoid malformation; intralobar pulmonary sequestration; extralobar pulmonary sequestration



DOI: https://doi.org/10.3941/jrcr.v11i4.3002