Sporadic Hemangioblastoma Arising from the Infundibulum

Authors

  • Michael Navid Pakdaman
  • Matthew J Austin
  • Serguei Bannykh
  • Barry D Pressman

DOI:

https://doi.org/10.3941/jrcr.v11i5.2981

Keywords:

Hemangioblastoma, von-Hippel-Lindau disease, suprasellar mass, infundibulum, neuroradiology, MRI

Abstract

Hemangioblastomas are rare vascular tumors most often found in the posterior fossa and cervical spinal cord and commonly associated with von Hippel-Lindau Disease. We report a case of sporadic hemangioblastoma in a patient without von Hippel-Lindau Disease. Imaging characteristics included a solid, suprasellar mass that was homogeneously enhancing. These findings most resembled a pituicytoma or choroid glioma because of the close association with the infundibulum and the homogeneous avid enhancement. Microscopically, the neoplasm was seen to be composed of vascular channels associated with foamy stromal cells, containing clear cytoplasmic vacuoles. Microscopic and immunohistochemical findings were consistent with hemangioblastoma. Hemangioblastomas are a rare form of vascular tumor most commonly associated with von-Hippel Lindau disease. Our finding of non-cystic hemangioblastoma arising from the infundibulum demonstrates that, while rare, hemangioblastomas should be considered on the differential diagnosis for an avidly enhancing suprasellar mass.

Author Biographies

Michael Navid Pakdaman

Resident physician at Cedars Sinai Medical Center. Graduation date 2019.

Matthew J Austin

Neuroradiology fellow at Cedars Sinai Medical Center

Serguei Bannykh

Faculty Pathologist at Cedars Sinai Medical Center

Barry D Pressman

Professor & Chair, Department of ImagingS. Mark Taper Foundation Imaging CenterCedars Sinai Medical Center8700 Beverly Blvd. Taper M-

Published

2017-05-27

Issue

Section

Neuroradiology