Rosai-Dorfman Disease Isolated to the Thoracic Epidural Spine

Authors

  • Benjamin Kozak
  • Jason Talbott
  • Alina Uzelac
  • Bhavya Rehani

DOI:

https://doi.org/10.3941/jrcr.v9i11.2629

Keywords:

Rosai-Dorfman, spine, thoracic, epidural, sinus histiocytosis with massive lymphadenopathy, histiocytic disease, MRI

Abstract

Rosai-Dorfman disease is a rare benign histiocytic disease that infrequently presents in the spine. We report a case of Rosai-Dorfman disease isolated to the epidural thoracic spine in a 26-year-old male. To our knowledge, this is the 15th reported case of isolated spinal disease and only the fourth case of isolated thoracic epidural disease.  Given its rarity as well as non-specific symptoms and imaging findings, Rosai-Dorfman disease is often not considered and misdiagnosed on imaging studies. To help improve awareness of Rosai-Dorfman spinal disease, we review the literature and discuss the epidemiology, clinical presentation, imaging features, and treatment considerations for this condition.

Author Biographies

Benjamin Kozak

Benjamin Kozak, BA is a medical student at the University of California, San Francisco.

Jason Talbott

Jason Talbott, MD, PHD is an Assistant Professor in the Department of Radiology and Biomedical Imaging at the University of California, San Francisco and San Francisco General Hospital.

Alina Uzelac

Alina Uzelac, DO is an Assistant Professor in the Department of Radiology and Biomedical Imaging at San Francisco General Hospital.

Bhavya Rehani

Bhavya Rehani, MD is an Assistant Professor in the Department of Radiology and Biomedical Imaging at the University of California, San Francisco and San Francisco General Hospital.

Published

2015-11-25

Issue

Section

Neuroradiology