The quadricuspid aortic valve

The quadricuspid aortic valve

Arie Franco, Simon Gabriel, Stefan Georg Ruehm


The quadricuspid aortic valve is a very rare congenital defect that may be an isolated entity or associated with a multitude of cardiovascular abnormalities. Isolated cases usually manifest late in life with the complication of aortic regurgitation, which can be delayed by early valve replacement. We present a case of quadricuspid aortic valve associated with truncus arteriosus, ventricular septal defect, and interrupted aortic arch.


Quadricuspid aortic valve; Heart; Truncus Arteriosus; Cardiac valves; cardiac Magnetic resonance Imaging