Multisystemic Langerhans Cell Histiocytosis with advanced lung involvement

Authors

  • Ricardo Andrade Fernandes de Mello
  • Joana Waked Tanos
  • Melissa Bozzi Nonato Mello
  • Edson Marchiori

DOI:

https://doi.org/10.3941/jrcr.v6i11.1130

Keywords:

Langerhans cell histiocytosis, computed tomography, lung, skin diseases

Abstract

Langerhans cell histiocytosis is a rare disease of unknown cause, characterized by the proliferation of histiocytic cells (Langerhans cells), that can sometimes be especially difficult to diagnose due to its wide clinical spectrum, ranging from a single lesion to a multisystemic disorder. Appropriate disease staging is fundamental, since treatment depends upon the severity of the disease, and imaging methods play a fundamental role not only in diagnosing and assessing the extent of Langerhans cell histiocytosis, as well as guiding the appropriate treatment for the patient and their monitoring.

Author Biography

Ricardo Andrade Fernandes de Mello

Department of Radiology

Professor of Radiology, MSc

Published

2012-11-19

Issue

Section

Thoracic Radiology